MALNUTRITION / MedUrgent

 

MALNUTRITION





 Introduction

Nutrition is the process by which the organism utilizes food. The purpose is to maintain life, growth, normal functioning of organ, energy, and reproduction of species.

Malnutrition is any form of disordered nutrition with a span from obesity to Protein Energy Malnutrition (PEM). The latter can be endogenous due to of utilization, or exogenous due to defective intake or both.

The PEM is range of pathological conditions arising from coincident lack in varying of protein and calories, occurring most frequently in infants and young children and commonly associated with severe recurrent infection. PEM includes a variety of closely related syndromes resulting from different deficiencies of calories and /or protein and is governed by the age of the child and severity and duration of the deficiency. The typical severe forms of PEM are known as Kwashiorkor and Marasmus, however, intermediate or combined forms in different stages of development are also observed. In all these conditions, there is low weight for age and low weight for height. Kwashiorkor is characterized by oedema and low body weight for age. It occurs commonly in the age group 1-3 years. Signs commonly seen include muscle wasting, dermatitis, hepatomegaly, hair changes, diarrhea and mental changes Marasmus is characterized by very low body weight for age, loss o subcutaneous fat, gross muscle wasting and absence of oedema. It occurs commonly in infants and very young children, although it may occur age and any society. Etiology:

• High protein and energy requirement of the rapidly growing child.

• Ignorance of parents concerning food needed by the growing child.

• Starvation: insufficient amount of food given due to unavailability, poverty, wrong believes, famine, food faddism and taboos (a practice based on wrong believes, Customs or religious grounds).

• Prolonged exclusive breast feeding with inadequate intake

• In availability or high cost of breast milk substitutes and use of over diluted Cow's or formula milks.

• Use of thin gruels made out of cereals or starchy products e.g. Cocked or wheat flour


• Stopping food from children during diarrheal diseases with the concept that food increases the duration and and frequency of the disease.

• Early weaning of young infants without alternative or adequate resources for safe alternative artificial feeding.

• Poor distribution of available food within the family.

• Acute infections such as measles, whooping cough and others that have direct effect on weight loss

• Prematurity

•Chronic disease which are common problems particularly in the developing world

•Congenital malformations, metabolic and endocrine disorders

 

EPIDEMIOLOGY

1. Infections lead to PEM directly due to reduced food intake during disease. Loss of appetite and stomatitis. Moreover, diarrhea leads to decreased absorption and increased loss of nutrients and pyrexia leads to high energy expenditure.

2. Low socioeconomic development of the country and that of the family

3.Low level of education of the parents, particularly the mother that leads to uneven distribution of available family financial and other resources, and family priorities include expenses' other than food.

4. Poor environmental sanitation

5. Ignorance that pre-school children have higher nutritional requirements for body weight; in addition to their increased incidence of diseases. They are commonly given less food to satisfy their nutritional needs for different reasons.

6. Feeding and weaning practices. are major contribute including early weaning practice milk substitutes , supplementation with over-diluted milk and poor quantity and quality of food supplements lead to severe malnutrition , Failure of breast feeding may be precipitated by psychological factors of the mother including painful suckling of the infant due to cracked or retracted nipple and breast infection. Additional factors include responsibilities of the working mother, anxiety and the desire to achieve a "modern lady". a Worse additional factor is speared of media advertisements regarding types of artificial milks, foods and also body style!


PATHOPHYSIOLOGY

Malnutrition occurs as a result of many other factors in the body ir to the above mentioned; these include disturbances in:

1. Water, electrolytes and minerals: Decreased osmolality, decreased glomerular filtration rate and impaired renal response to overload of water. Total body sodium, potassium and magnesium are reduced.

2. Carbohydrates: Hypoglycemia may occur and it is one of the causes of death in severe malnutrition due to:

• Impaired glucose absorption and metabolism

• decreased insulin level with poor response to intravenous glucose, decreased gluconeogenesis. Decreased G-6-Phosphatase in the liver leading to failure of breakdown of glycogen to glucose

• Decreased disaccharides level in the intestinal mucosa leads to accumulation of sugars and water in the intestinal lumen that can lead to osmotic diarrhea.

3. Hormonal disturbances:

Low thyroid functions compared to normal children, but this is thought to be due to adaptation as there is no functional impairment upon stimulation High level of Growth Hormone High level of plasma epinephrine

• High level of plasma Cortisol

4. Fats:

• Colonization of proximal part of the small intestines with bacteria high levels of free bile acids and failure of esterification and on of fat. Free fatty acids may distort the intestinal villi

• Decreased pancreatic lipase

• Decreased ß-lipoprotein formation in the liver leads to failure of fat from the liver to other organs

• Decreased Retinol-binding protein leads to accumulation of vitamin A in the liver and results in low serum vitamin A

• Development of fatty liver due to increased fat transport from adipose tissue, increased liver lipogenesis and decreased B-lipoprotein synthesis

 

5. Protein and Amino Acids:

• In bwashiorkor, hypoproteinemia due to hypoalbuminemia resulting from decreased synthesis

• Low B-globulin and Increased level of a1, a2-globulins and y-globulins • low plasma amino acids except phenylalanine .

• Loss of fecal nitrogen during diarrhea Decreased urea synthesis

Biochemical changes:

 A. Serum protein and albumin:

• Serum albumin level is <_ 3 gm/100ml (a reduction of _> 20% of serum albumin indicates early malnutrition) and the albumin/globulin ratio is low. During recovery, the albumin level rises early before changes in the clinical picture and can be used as an indicator

• B-globulins level decreases while y-globulin rises

• Both transferrin and pre-albumin are reduced early.

B. Amino acids:

• Essential amino acids are reduced especially the branched chain amino acids (except phenylalanine and lysine), while non-essential amino acids are not affected or raised

C. Glucose:

°May be decreased to _< 30mg% in severely malnourished children.

 D. Urine: 

The hydroxyproline Index which is measured according to the following equation: (umol Hydroxyproline/ml) / (umol Creatinine/ml/kg)

The urinary Hydroxyproline excretion is an indicator of growth in children the index is markedly reduced in PEM.

Age is excluded from the Index because it is usually unknown in poor unities and therefore, the test is not age-dependent. 

• Creatinine excretion decreases with the decrease of muscle mass:

• creatinine clearance per square meter surface area equals height (m) x 0.43 serum creatinine: Normal range is 80-120 mg E. Water and Electrolytes: Total body water is increased in both kwashiorkor and marasmus though there may be evidence of dehydration.

 • Total body Sodium is raised; Total body Potassium is low and total body Magnesium is low and this may lead to rigidity or convulsions F. Acid Base Balance:

• There is a compensated hyperchloremic acidosis with normal pH hich Chloride and low CO2 Pathology: 

Pathological changes that are commonly seen in PEM include:

Hair and skin changes:

In Kwashiorkor, the hair is silky, sparse and easily pluckable. Areas of hypopigmentation corresponding to the periods of deficiency (flag sign). The skin shows areas of erythema, and areas of hypopigmentation, hyperpigmentation, excoriation and hyperkeratosis. Skin may atrophy and there are areas which peel off easily (flaky paint rash), and secondary infection may occur.

• Fat:

Preserved in Kwashiorkor and consumed by lipolysis and gluconeogensis in Marasmus. 

- Muscles: Are atrophied, and this is related to energy deficit.

• Gastrointestinal Tract: In kwashiorkor, atrophy of intestinal mucosa is minimal where the villous size is reduced and villi are both normal and slightly reduced, while in marasmus villi are short and there is also atrophy of brush boarders. Decreased levels of intestinal disaccharides, dipeptidases and lipases have been documented

• Liver: Fatty changes in kwashiorkor, starts in periportal areas and then spreads centrally. This is reversible with nutritional treatment.

• Pancreas: There is atrophy of acini and loss of zymogens granules. Decrease of endocrine and occasionally exocrine secretions which are reversible with treatment.

· Urinary Tract: tubules Hyalinization of glomeruli and fatty degeneration of the convoluted tubules

• Thymus: 

Is atrophied and there may be fatty degeneration of lymphoid tissue

. Hormonal changes

Thyroid gland: Severe forms of PEM may lead to decreased levels of thyroxin-binding globulin (TBG) and thyroxin-binding pre-albumin (TBPA). Prolonged PEM leads to sluggish feedback mechanism between thyroxin level and TSH.

Moderate hypoglycemia is commonly seen in all forms of PEM during infection and hypothermia.

Low BMR is due to deficiency of diet and not thyroxin.

Insulin: PEM is associated with impaired insulin release resulting in impaired glucose tolerance test. Raised levels of plasma fatty acids and growth hormone lead to normal or high levels of blood glucose through gluconeogenesis.

The role of glucagon is not yet defined.

Adrenal glands may become smaller in size and hormone output and metabolism are slowed down and the levels of steroids could be normal or high. Urinary steroids excretion is low and rate of degradation of cortisol is impaired.

Aldosterone level is raised leading to hypokalemia There is marked sodium loss in urine because of decreased reabsorption and inappropriate ADH secretion.

Pituitary: The feedback of Hypothalamic-pituitary axis is essentially normal, though slow.

 

• Immune System

1-Humoral Immunity: B cells number is normal or elevated IgA, IgG, IgM levels in the circulation are normal or elevated. Secretory IgA level is reduced leading to increased susceptibility to gram negative bacterial infections of the respiratory system and gastrointestinal tract. IgE and IgD levels are elevated.

Antibody response to Yellow Fever vaccine, Typhoid vaccine and Influenza Vaccine is impaired; however, the antibody response to antigens of Measles, Poliomyelitis, Tetanus and Diphtheria Toxoid is normal Complement proteins are all decreased except C4

2-Cellular Immunity: Thymus is atrophic with fibrous tissue replacing its normal lymphoid tissue and Hassel's corpuscles.

  peripheral lymph nodes and spleen may become atropnic There is delayed cutaneous hypersensitivity e.g. BCG vaccination There is decreased number and depressed responsiveness of thymus dependent (T) Lymphocytes.

Chemotaxis, phagocytosis and degranulation of polymorphs are normal but the killing function is defective.

Enzymes of polymorphs (pyrovate kinase and peroxidase) are normal.

Normal resting reduction of NBT dye test

Synergism of PEM and infectious diseases

Effect of malnutrition on infections

• Deficient intake of protein and micronutrients adversely affect body defense mechanisms. • Protein deficiency leads to poor wound healing, poor fibroblastic response to trauma, poor abscess wall development, poor collagen formation and poor antibody formation.

• Vitamin A deficiency leads to decreased macrophage activity, decreased activity of lysozymes in tears, sweat, saliva and body fluids and disturbed tissue and mucus protective mechanisms.

• Vitamin B deficiency leads to decreased antibody formation, decreased macrophage activity and decreased interferon formation. • Vitamin C deficiency leads to decreased hydroxyproline formation resulting in poor collagen formation and poor wound healing.

 
Effect of infection on nutritional status: 

• Infection and stressful conditions adversely affect the nutritional status by loss of appetite and decreased tolerance to food.

• The tendency to change the patient diet during disease from solid to liquid leads to decreased amount of protein taken.

• Fever and stressful conditions leads to high BMR, loss of nutrients sweat and excess nitrogen excretion in urine.

• Stressful conditions lead to high insulin and cortisone secretion, increase gluconeogenesis from body proteins.

• During infection, vit.A level is lowered and may precipitate xerophthalm

• During infection there is loss of Na, K, Mg and CI.

•Chronic infection leads to simple chronic anemia. hook worm leads iron deficiency anemia and viral infections can precipitate pancytopenia

•Diarrhea leads to loss of nutrients in stools and decreased absorption of fat.


CLASSIFICATION OF PEM

Classification of PEM (originally called Protein-calorie malnutrition by lelliffe D.B. in 1959), differs according to the objectives to be achieved. A quantitative classification that is suitable for field studies might not fulfill the requirement of a qualitative clinical study where the type, severity and duration of the condition are important. An acceptable classification must be simple, practical and applicable in different areas used by different workers. The most widely used index in PEM classification is weight for age as it indicates the condition of the child compared to a standard at the same age. However it is not always possible to obtain the exact age especially in poorer illiterate societies. Weight for height is an index of the current nutritional status and is often used in surveys. Height for age gives a picture of the past nutritional history; accordingly, descriptive terms like stunting (deficit in height for age) and wasting (deficit in weight for height) are used. No classification, so far, is ideal because it is impossible to define "normal"; instead, the "Reference Standard” is used.

 

1. Gomez's classification (1956): using Harvard fiftieth percentile as a standard

First degree PEM: 90- 75% centile

Second degree PEM: 75-60% centile

Third degree PEM: less than 60% centile

2. Jelliffe classification (1966): (using Harvard fiftieth percentile as a standard)

First degree : 90- 80% centile

Second degree : 80- 70% centile

Third degree : 70-60% centile

Fourth degree : less than 60% centile

3. Garrow's classification (1966): (using Harvard fiftieth percentile as a standard)

Kwashiorkor: wt. 70 -60% +oedema +hepatomegaly or dermatosis

Marasmus: Wt. 560% no oedema or hepatomegaly or dermatosis Marasmic kwashiorkor: Wt._< 60% + oedema hepatomegaly or dermatosisŲ²







Laboratory Tests:

1. Blood glucose: <54mg/dl indicates hypoglycemia

2. Blood film for malaria should be done in endemic areas

3. Hemoglobin: <4gm/dl indicates very severe anemia

4. Packed cell volume: <12% indicates very severe anemia

5. Urine general and culture: Presence of bacteria on microscopy or culture

(or 10 leucocytes per high power field) indicates infection

6. Stools microscopy: Blood for dysentery and giardia cysts or trophozoites for infestation

7. Chest x-ray: patchy pneumonic consolidations (pneumonia), pulmonary congestion (heart failure) and rachitic changes in bones

8. Mantoux Test: Often negative


MANAGMENT

1. Hypothermia: If child's rectal temperature is <35.5 C (95 F), the child should be put in a Kangaroo position on mother's chest and actively warmed by proper covering and heating.

2. Hypoglycemia: If child's blood glucose is <3 mmol/, a bolus of 10% glucose or sucrose (oral or NG) should be given. If blood glucose <3 mmol/l and the patient is lethargic, unconscious or convulsing, sterile 10% glucose should be given intravenously in a dose of 5ml/kg; and 50 ml bolus by NG tube should be administered. Alternatively, you can use 25%Dextrose (2ml/kg) or 50%Dextrose (1 ml/kg)

3. Anemia: If Hb. <40gm/l or PCV <12%, either whole fresh blood in a dose of 10ml/ kg or 5-7 ml/kg packed cells should be given slowly over 3 hours.

4. Eye signs: If the patient has purulent conjunctivitis evidenced by pus, redness or swelling of the eye, this should be treated by chloramphenicol drops or tetracycline ointment in addition to atropine drops. Prophylactic dose of oral vitamin A drops or tablets is given according to age. If there are Bitot spots or ulcerations, give vitamin A in therapeutic doses on day 1, 2, 14 Vitamin A dose according to age is as such:50 000 IU for those <6 months; 100 000 IU for patients aged 6 - 12 months and 200 000 IU for patients older than 12 months.

5. Feeding: Nutritional treatment is divided into 3 phases:

Phase I: (Initiation phase)

As severely malnourished children cannot handle large quantities of dietary protein, fat or Na, feeding is commenced by F-75 formula (i.e. low energy and low protein) as soon as possible. If the child is dehydrated. rehydrate initially and the patient is reweighed before determining the amount of feeds. An NG tube may be used if the child cannot complete the calculated amount. Night feeds are important to prevent hypoglycemia and feeds are given 2 hourly. If hypoglycemia is determined by a random blood sugar, then feeding should be 14 of this amount given every half hour for the first 2 hours, and continue this regimen until blood glucose reaches 3 mmol/l.

Phase 2: (Transition phase) When the appetite returns, oedema starts to subside, and the medical complications are treated and this usually takes about 3 days or more, feeding with F-100 formula (i.e. high energy and high protein) should be offered and given according to body weight. Feeds should be increased by 10 ml until patient refuses. The patient should be weighed daily and monitored for signs of fluid overload and heart failure.

Phase 3: (Rehabilitation phase) Once the child tolerates large amounts of feeds, referral to an nutrition rehabilitation center is indicated where his weight is every 2 weeks, health education regularly given, and monitoring is done.

6. Shock:

 If there are signs of shock including lethargy, unconsciousness, cold hands, slow capillary refill >3 seconds or has weak fast pulse, administration of IV normal saline or Ringer's lactate in of 15 ml/kg in one hour should be started immediately. If there is no improvement, the same amount should be repeated until signs of shock disappear. This is followed by giving alternate ResoMal and F-75 for up to 10 hours.

If there is no improvement on IV fluids, the patient should be transfused with whole fresh blood (10ml/kg) given in a relatively fast rate. 7. Dehydration: Treatment of severe dehydration should be commenced using IV normal saline or Ringer's lactate infusions according to weight until it disappears. This is followed by ReSoMal by NG tube in a dose of 5 ml/kg every 12 hour for 2 hours, thereafter on alternate hours and in addition F-75 liquid formula should be given in a similar dose. 8. Dermatosis:

If there is evidence of severe dermatosis, the patient should receive a bath with 1% potassium permanganate solution, or Gentian violet solution may be applied on the skin. If there is fungal infection, Nystatin is added. Oral zinc solution can speed up recovery (10mg/day for 10 days).

Management of Malnutrition in infants

Infants less than 6 months of age and children with body weight of s 4kg are treated separately, though the same rules of phase management are applied.

At this age group malnutrition may result from lack of breast feeding inadequate breast feeding or failure of breast feeding due to congenital malformations or developmental problems. Indications for hospital admission Include visible wasting (SD Score cannot be applied to this age group), bilateral pitting oedema and failure of breast feeding.

Start with dilute F100, but if there is oedema, start with F75. Dilute F100 is formed of one sachet of powder (one liter size) and add water to make 1350ml. volume to be given in the Initial Phase is 130ml/kg/day and should be increased regularly by 5 ml/feed if the infant is accepting and finishing the offered feed or not gaining wieight properly. Supplementary Suckling Technique i.e. breast feeding and formula feed together, offers the infant a good amount of milk as well as keeps breast feeding continuity. Nasal tube should be avoided unless the infant is not taking enough and always at resuming full breast feeding as soon as possible. Add one dose of prophylactic vitamin A (50,000 I.U) and folic acid 2.5 mg as a single dose. If antibiotics are needed; use Amoxicillin (30 mg/kg/12 Hrs.) and Gentamycin (7.5 mg/kg/day). Infants can be discharged when the daily weight gain is 20 grams or more, oedema disappeared and there are no medical complications


Phenomena encountered during the Rehabilitation phase

These phenomena are not very well understood, however micro- and macronutrient imbalance play an important role in their appearance

1-Pseudotumor Cerebri: Presents with clinical picture of increased intracranial pressure with normal ventricular size, anatomy and position

2-Encephalitis-like syndrome: Presents with unexplained drowsiness and loss of consciousness

3-Rickets: Presents with clinical picture of rickets as bones start to grow as bones start to grow

4- Kahn Syndrome: the syndrome presented with Parkinsonism-like picture (tremors, rigidity, bradykinesia and myoclonus) around the 6th day after the day after therapy.

5-Micronutrient Deficiency Presents with clinical picture of specific micronutrient deficiency e.g. zinc vit E, SELENIUM....

6-Anemia: Presents with a blood picture of hypochromic microcytic, megaloblastic or dimorphic anemia

7-Gomez Syndrome: Presents with clinical picture of a decompensating liver (hepatomegaly, ascites, collaterals, parotid enlargement, hypertrichosis, gynaecomastia and eosinophilia) Each might need relevant or specific treatment as the clinical picture dictates.

   

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